Boari Flap Ureteroneocystostomy in the Management of Primary Localized Amyloidosis of the Ureter

Amyloidosis is the deposition of insoluble protein in the extracellular space, which is more commonly systemic. Localized amyloidosis of the ureter is a rare entity and is often confused with urothelial malignancy. Here, we present the case of a 64-year-old male who presented with left flank pain, and contrast contrast-enhanced computed tomography scan revealed a distal ureteric enhancing lesion. Ureteric biopsy revealed the diagnosis of ureteric amyloidosis, which helped guide the definitive management-excision of the affected ureteric segment, followed by reconstruction with a Boari flap. The preoperative biopsy confirming amyloidosis helped avoid a radical surgery with the suspicion of a urothelial malignancy.