Bilateral Localised Primary Ureteric Amyloidosis

Amyloidosis is a group of diseases in which insoluble proteins called amyloids deposit in tissues and cause problems with body functions. It is not a form of cancer but is a serious condition. It may be symptomatic or localized. The latter is a rare condition and the affection of the ureter has been reported in fewer than 50 cases so far. This case is unique because of its presentation with features of a urothelial tumor of the upper tract and bilateral involvement of the ureter. The affection of the ureters was separated by more than a decade. Given the knowledge gained after treating the first lesion, it was possible to anticipate and suspect a similar lesion affecting the other ureter. A conservative and reconstructive surgery was performed with gratifying results.