Different responses to exercise between Andersen–Tawil syndrome and catecholaminergic polymorphic ventricular tachycardia

51 patients with inherited arrhythmic disorders characterized by bidirectional ventricular tachycardia, comprising 26 Andersen-Tawil Syndrome (ATS) patients with KCNJ2 mutations (from 22 families) and 25 catecholaminergic polymorphic ventricular tachycardia (CPVT) patients with RyR2 mutations (from 22 families).

Exercise stress testing

Comparison between ATS and CPVT patient responses

Responses of ventricular arrhythmias (VAs) to exercise testing and the morphology of VAssurrogate