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May 16, 2026Indian Pediatrics Case ReportsOpen Access

Juvenile Dermatomyositis with Systemic Capillary Leak Syndrome Complicated by Disseminated Aspergillosis: A Case Report

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Authors

GMGranthana MandalInstitute of Child Health PGPrabhas Prasun GiriInstitute of Child Health KMKaushik MaulikInstitute of Child Health

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Implication

Case report reveals severe outcome in juvenile dermatomyositis with systemic capillary leak syndrome, suggesting need for caution with immunosuppression.

Key Points

To describe a complex case of juvenile dermatomyositis with systemic capillary leak syndrome and its fatal complications.
Detailed clinical assessment of an 8-year-old girl presenting with multiple symptoms and significant lab findings.
Management included high-dose immunosuppression, fluid resuscitation, mechanical ventilation, and kidney support therapy.
Investigations included MRI, serology testing for autoimmune markers, and monitoring for opportunistic infections.
The child presented with severe symptoms including hypotension, muscle weakness, and hypotonic edema, requiring aggressive supportive measures.
Despite initial treatment, she developed severe opportunistic infections, including Acinetobacter pneumonia and disseminated aspergillosis.
The case emphasizes the risks associated with prolonged immunosuppression, which ultimately contributed to her death from pulmonary hemorrhage.

Cite This Study

Mandal et al. (2026) studied this question.

synapsesocial.com/papers/6a080ab3a487c87a6a40ca71 https://doi.org/10.4103/ipcares.ipcares_287_25

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Implication

Case report reveals severe outcome in juvenile dermatomyositis with systemic capillary leak syndrome, suggesting need for caution with immunosuppression.

Juvenile Dermatomyositis with Systemic Capillary Leak Syndrome Complicated by Disseminated Aspergillosis: A Case Report

Discussion

Member takes

Implication

Key Points

Cite This Study

Juvenile Dermatomyositis with Systemic Capillary Leak Syndrome Complicated by Disseminated Aspergillosis: A Case Report

Discussion

Member takes

Implication

Key Points

Cite This Study

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