Key result
Radiofrequency ablation successfully treats atrial flutter to maintain sinus rhythm in an AMA-positive myositis case.
Case Report (n=1)
No
This case highlights that cardiac involvement such as atrial flutter can occur in AMA-positive myositis and may require radiofrequency catheter ablation for rhythm control.
AMA-positive myositis with atrial flutter may require ablation for rhythm control; single case leaves open prevalence and screening needs.
We report a 55-year-old man who experienced proximal muscle weakness accompanied by the atrial flutter (AFL) with 1:1 conduction. Detailed examination revealed elevated antimitochondrial antibodies (AMA) and creatine kinase (CK). AFL was converted to sinus rhythm by cardioversion. He was diagnosed as AMA-positive myositis-associated AFL and was treated by prednisolone. Although his muscle weakness and CK level improved, AFL with 1:1 conduction reappeared. Therefore, radiofrequency catheter ablation (RFCA) was needed to treat the AFL, resulting in maintenance of sinus rhythm. This case report describes cardiac involvement in a patient with AMA-positive myositis.
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Yamanaka et al. (2017) conducted a case report in Antimitochondrial antibodies-positive myositis with cardiac involvement (n=1). Prednisolone and radiofrequency catheter ablation was evaluated on Clinical improvement. In a 55-year-old man with antimitochondrial antibodies-positive myositis, prednisolone improved muscle weakness, but radiofrequency catheter ablation was required to treat atrial flutter and maintain sinus rhythm.
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