Key result
Valve-sparing replacement of the aortic root, ascending aorta, and aortic arch was successfully performed in a 2.5-year-old boy with Loeys-Dietz syndrome.
Why the study?
Does valve-sparing operation (VSO) of the aortic root successfully treat aortic root aneurysm in a young patient with Loeys-Dietz syndrome?
Case Report (n=1)
Does valve-sparing operation (VSO) of the aortic root successfully treat aortic root aneurysm in a young patient with Loeys-Dietz syndrome?
Valve-sparing operation of the aortic root can be successfully performed in very young children with Loeys-Dietz syndrome to avoid prosthetic valve replacement.
May support valve-sparing aortic surgery in toddlers with Loeys-Dietz syndrome; leaves open durability and generalizability.
We describe a successful surgical treatment in a 2.5-year old boy with Loeys-Dietz syndrome, in whom we performed aortic arch and ascending aorta replacement with a valve-sparing operation (VSO) of the aortic root because of significant aortic insufficiency and dilation of the aortic root. We believe that VSO is ideal for treating young patients with aortic root aneurysm with normal or minimally diseased aortic cusps to avoid the disadvantages of prosthetic valve replacements.
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Özker et al. (2012) conducted a case report in Loeys-Dietz syndrome with aortic root aneurysm and aortic insufficiency (n=1). Aortic arch and ascending aorta replacement with a valve-sparing operation (VSO) of the aortic root was evaluated. Valve-sparing replacement of the aortic root, ascending aorta, and aortic arch was successfully performed in a 2.5-year-old boy with Loeys-Dietz syndrome.
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