A Case of Unresectable Pulmonary Artery Intimal Sarcoma with Prolonged Survival by Chemotherapy

Figures

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  Fig. 1.. Imaging studies by MRI. (a) MRI at onset showed a lesion in the main pulmonary artery extending to the right and left pulmonary arteries. (b) One and half cycles of first-line paclitaxel treatment resulted in shrinkage of the tumor tail extending to the right pulmonary artery. (c) At 3.5 months, the tumor in the left pulmonary artery showed progression. (d) At 8.0 months, the tumor in the left pulmonary artery showed further progression.

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  Fig. 2.. Pathological studies. (a) Left–Histologically, the tumor cells showed a pattern of soft tissue sarcoma. On immunohistochemical analysis, they were negative for cytokeratin AE1/AE3, smooth muscle actin, desmin, caldesmon, S-100, and CD34. Right–Fifty percent of the tumor cells were positive for Ki-67. (b) Tumor cells in the skin nodule resected at 13 months after onset were histologically diagnosed as soft tissue sarcoma.

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  Fig. 3.. Imaging studies by CT. (a) CT at onset showed multiple lung nodules (arrow). (b) After three cycles of first-line paclitaxel treatment, most of the lung nodules disappeared.