Key result
A Fontan operation was successfully performed in a 4-year-old boy with a history of Takotsubo cardiomyopathy, with no signs of recurrence over the subsequent 2 years.
Case Report (n=1)
A Fontan operation can be successfully performed in a paediatric single-ventricle patient with a history of Takotsubo cardiomyopathy without recurrence over 2 years.
May support Fontan in select children with resolved Takotsubo cardiomyopathy; leaves open generalizability and long-term safety.
Takotsubo cardiomyopathy is very rare in the paediatric population and has not been described in a single-ventricle patient yet. We report the case of a 4-year old boy with a history of Takotsubo cardiomyopathy in whom we performed a Fontan operation. After coil embolization of the minor aortopulmonary collateral arteries, the patient developed Takotsubo cardiomyopathy. His cardiac function largely recovered over 3 months. He subsequently progressed to a Fontan operation and was weaned uneventfully off cardiopulmonary bypass, on minimal doses of dopamine and milrinone; he was sedated using a dexmedetomidine infusion and a midazolam bolus. There were no signs of recurrent Takotsubo cardiomyopathy over the subsequent 2 years.
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Watanabe et al. (2014) conducted a case report in Takotsubo cardiomyopathy in a single-ventricle patient (n=1). Fontan operation was evaluated on Recurrent Takotsubo cardiomyopathy. A Fontan operation was successfully performed in a 4-year-old boy with a history of Takotsubo cardiomyopathy, with no signs of recurrence over the subsequent 2 years.
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