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June 17, 2026Journal of Clinical MedicineOpen Access

Cardiovascular Involvement in Erdheim–Chester Disease Presenting as Pericardial Tamponade: A Case Report and Multimodality Imaging Review

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Authors

FSFrancesco Di SpignoAFAndrea FaggianoARAlfredo Ricchiuto

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Overview

Case report reveals cardiac symptoms in Erdheim-Chester Disease, suggesting critical diagnostic pathways.

Key Points

  • This report aims to highlight the cardiovascular manifestations of Erdheim-Chester Disease and the imaging modalities needed for its diagnosis.
  • Case report of a 58-year-old patient presenting with exertional dyspnoea and fatigue.
  • Multimodal imaging approaches included CT, PET, MRI, and X-ray assessments to evaluate cardiac involvement.
  • Analysis focused on imaging findings related to pericardial effusion and aortitis.
  • The imaging revealed a significant circumferential pericardial effusion and findings consistent with aortitis.
  • Cardiovascular involvement was identified as a common occurrence, affecting at least 40% of ECD patients.
  • The findings underscore the importance of early multimodal imaging for accurate diagnosis of ECD.

Cite This Study

Spigno et al. (2026) studied this question.

synapsesocial.com/papers/6a323bbcd50b63ecad20639ahttps://doi.org/10.3390/jcm15124650
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Also Consider

Synapse has enriched 5 closely related papers on similar clinical questions. Consider them for comparative context:

  1. 1Erdheim‑Chester disease of multisystem involvement with delayed diagnosis: A case report and literature review2024 · 2 citations
  2. 2Erdheim-Chester Disease presenting with constrictive pericarditis: A case report and review of the literature2024 · 2 citations
  3. 3Case Report: Relapsing pleural effusions and coated aorta revealing Erdheim–Chester disease2025
  4. 4Erdheim-Chester disease: unveiling hidden manifestations through two case reports2025
  5. 5The Spectrum of Cardiac Involvement in Erdheim-Chester Disease is Broader than Previously Thought2024