Key result
A fetus with progressive right ventricular cardiomyopathy and functional tricuspid and pulmonary atresia was successfully managed postnatally with prostaglandin and inotropic infusions without surgery.
Why the study?
Cardiomyopathy is a rare diagnosis in the fetus that usually presents as a dilated, poorly functioning ventricle.
Case Report (n=1)
Prenatal functional tricuspid and pulmonary atresia due to progressive right ventricular cardiomyopathy can be successfully managed postnatally with medical therapy (prostaglandin and inotropes) without requiring surgery.
Rare fetal RV cardiomyopathy may cause functional atresia resolving without surgery; leaves open optimal prenatal surveillance and management strategies.
Cardiomyopathy is a rare diagnosis in the fetus that usually presents as a dilated, poorly functioning ventricle. We present the case of a fetus that developed functional tricuspid and pulmonary atresia due to progressive right ventricular cardiomyopathy. The baby was supported with prostaglandin and inotropic infusions after delivery, eventually weaning off without need for surgical intervention. This case illustrates the prenatal findings that evolved and the successful postnatal management.
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Patel et al. (2019) conducted a case report in Right ventricular cardiomyopathy with functional tricuspid and pulmonary atresia (n=1). Prostaglandin and inotropic infusions was evaluated on Successful weaning off support without surgical intervention. A fetus with progressive right ventricular cardiomyopathy and functional tricuspid and pulmonary atresia was successfully managed postnatally with prostaglandin and inotropic infusions without surgery.
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