Key result
A 61-year-old male with a rare biventricular phenotype of arrhythmogenic cardiomyopathy was successfully diagnosed using the Padua criteria and treated with an implantable cardioverter defibrillator to prevent sudden cardiac death.
Why the study?
Arrhythmogenic cardiomyopathy mostly affects the right ventricle with most prior reports in young people, making biventricular phenotypes in older adults uncommon.
Case Report (n=1)
No
Highlights a rare presentation of biventricular arrhythmogenic cardiomyopathy in an older adult, successfully managed with an ICD.
May support ICD consideration in symptomatic biventricular arrhythmogenic cardiomyopathy; leaves open generalizability beyond this case.
Arrhythmogenic cardiomyopathy is a rare hereditary structural heart disease, with various phenotypes, which mostly affects the right ventricle of the heart, resulting in fibrofatty replacement of the heart muscles and a proclivity to create spontaneous malignant cardiac arrhythmias that may lead to sudden death. Most previous reports were noted on young people. We report a case of its biventricular phenotype in a 61-year-old heavy truck driver who has a current medical history of diabetes mellitus and smoking and was incidentally diagnosed based on the Padua criteria after presenting to the hospital with complaints of lightheadedness and syncope. He eventually had an implantable cardioverter defibrillator, hence preventing death. We were able to correctly diagnose the case and prevent sudden cardiac death by instituting the necessary management.
No takes yet. Share an insight, caveat, or question.
Aiwuyo et al. (2022) conducted a case report in Arrhythmogenic Cardiomyopathy (biventricular phenotype) (n=1). Implantable cardioverter defibrillator (ICD) was evaluated. A 61-year-old male with a rare biventricular phenotype of arrhythmogenic cardiomyopathy was successfully diagnosed using the Padua criteria and treated with an implantable cardioverter defibrillator to prevent sudden cardiac death.
Synapse has enriched 5 closely related papers on similar clinical questions. Consider them for comparative context: