Why the study?
Primary adrenal angiosarcoma is a rare, aggressive malignant vascular neoplasm with a propensity for local recurrence and metastasis.
This report adds two cases of a rare, aggressive vascular neoplasm (primary adrenal angiosarcoma) occurring with synchronous adrenocortical adenomas to the literature.
Synchronous adrenocortical adenomas noted; leaves open whether this represents a true association or coincidence in this rare tumor.
Primary adrenal angiosarcoma is a rare, malignant, vascular neoplasm. These neoplasms typically arise in middle age (median age of 60 years) and are more common in males (65%) than in females. Although rare, these neoplasms are aggressive with a propensity for local recurrence and metastasis and a median survival of 18 months. We present 2 cases of primary adrenal angiosarcoma with synchronous, ipsilateral adrenocortical adenomas. We review the cases of adrenal angiosarcoma reported since 1988 and discuss their clinical and histopathologic characteristics.
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Ladenheim et al. (2021) studied this question.
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