Key result
A 41-year-old woman was diagnosed with a rare primary adrenal epithelioid angiosarcoma, highlighting the diagnostic challenges of this rapidly progressive tumor.
Why the study?
Primary adrenal angiosarcomas are exceedingly rare with a poor outcome, lack pathognomonic clinical or imaging features, and have histological overlap with other adrenal tumors.
Case Report (n=1)
This case report expands the sparse literature on primary adrenal epithelioid angiosarcomas to aid in understanding their diagnostic features and clinical behavior.
May aid recognition of rare adrenal angiosarcoma; hypothesis-generating for diagnostic criteria in atypical adrenal masses.
Primary adrenal angiosarcomas are exceedingly rare with a rapidly progressive clinical course and a poor outcome. Establishing the diagnosis can be challenging, and it is complicated by the fact that there are no characteristic clinical or imaging features that are pathognomonic for angiosarcoma. Histologically, they can overlap with other more commonly encountered adrenal tumors. Herein, we present an otherwise healthy 41-year-old woman diagnosed with a primary adrenal epithelioid angiosarcoma. We aim to expand the knowledge of the sparse literature existing on primary adrenal angiosarcomas to help better understand the diagnostic features, clinical behavior, and management of these rare tumors.
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Parisi et al. (2023) conducted a case report in Primary adrenal epithelioid angiosarcoma (n=1). A 41-year-old woman was diagnosed with a rare primary adrenal epithelioid angiosarcoma, highlighting the diagnostic challenges of this rapidly progressive tumor.
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