Why the study?
Does en bloc resection improve hematologic defects in a patient with cavernous hemangioma of the chest wall and Kasabach-Merritt syndrome?
Does en bloc resection improve hematologic defects in a patient with cavernous hemangioma of the chest wall and Kasabach-Merritt syndrome?
En bloc resection of a chest wall cavernous hemangioma associated with Kasabach-Merritt syndrome successfully normalized preoperative hematologic defects.
May support resection for hematologic correction in this rare syndrome; hypothesis-generating and requires prospective validation.
A case report of an 18-year-old girl with a cavernous hemangioma of the chest wall is presented. Preoperatively, hematologic study revealed thrombocytopenia, hypoprothrombinemia, defective clot retraction, and increased bleeding time. Retrograde arteriography revealed that the vascular supply of the lesion originated from the left fifth to the tenth intercostal artery. It was felt that the symptoms and findings were similar to those described for the Kasabach-Merritt syndrome. The lesion and the chest wall were successfully resected en bloc. Six days postoperatively the preoperative hematologic defects had all returned to normal levels. A discussion of the Kasabach-Merritt syndrome and of the relationship of the coagulation defects to the lesion are presented.
No takes yet. Share an insight, caveat, or question.
Charles Fineberg (1963) studied this question.
Synapse has enriched 2 closely related papers on similar clinical questions. Consider them for comparative context: