Reports a rare case of aortic dissection in a young patient with both Marfanoid features and Ebstein anomaly.
May prompt aortic dissection consideration in acute abdomen for extended-survival MFS; leaves open potential Ebstein's co-occurrence links.
Background: Marfan syndrome is an autosomal dominant connective tissue disorder characterized by a combination of clinical manifestations in different organ systems. Patients with Marfan syndrome (MFS) whose lifetimes are extended may be encountered as acute abdomen cases (Aortic dissection) apart from the obligatory reasons and emergencies arising naturally out of their disease, as in the case reported. Ebstein's anomaly is a rare congenital heart disease; in which there is a downward displacement of the tricuspid valve into the right ventricle.
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Naresh Sen (2016) studied this question.
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