Why the study?
Primary pulmonary synovial sarcoma is a highly uncommon, high-grade malignant mesenchymal tumor with poor prognosis.
This case series highlights the clinical presentation and multimodality management of rare primary pulmonary synovial sarcomas.
Raises awareness of rare primary pulmonary synovial sarcoma; leaves open optimal multimodality strategies pending larger series.
Synovial sarcoma is a rare malignant mesenchymal tumor that can develop at any anatomic site. Pulmonary sarcomas constitute 0.1–0.5% of all primary lung malignancies. Primary pulmonary synovial sarcoma is highly uncommon. Most of the patients present with large intrathoracic masses with complaints of cough, chest pain, shortness of breath, or hemoptysis. Multimodality treatment in the form of wide excision, chemotherapy, and radiotherapy is the mainstay of therapy. Synovial sarcoma is considered a high-grade tumor with a poor prognosis. We hereby present three cases of histologically proven synovial sarcoma with predominantly pulmonary involvement, along with their management and in hospital outcome.
No takes yet. Share an insight, caveat, or question.
Peter et al. (2022) studied this question.
Synapse has enriched 5 closely related papers on similar clinical questions. Consider them for comparative context: