Key result
A unique phenotype of hypertrophic cardiomyopathy with right ventricular outflow tract obstruction in conjunction with left ventricle intracavitary obstruction is discussed.
Case Report
Highlights a rare phenotype of hypertrophic cardiomyopathy involving both right ventricular outflow tract and left ventricular intracavitary obstruction, for which specific management guidelines are currently lacking.
Rare dual-obstruction HCM phenotype lacks management guidelines; leaves open optimal therapy and natural history.
Obstruction of the right ventricular outflow tract (RVOT) is a rare finding in hypertrophic cardiomyopathy (HCM) patients unlike left ventricular outflow tract (LVOT) obstruction. Although there are guidelines that aid in clinical decision making in patients with LVOT obstruction, there are none addressing RVOT obstruction. As RVOT obstruction may pose serious clinical implications similar to LVOT obstruction, appropriate medical and surgical management is very important. A unique phenotype of HCM with RVOT obstruction in conjunction with left ventricle (LV) intracavitary obstruction is discussed.
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Malik et al. (2014) conducted a case report in Hypertrophic cardiomyopathy with right ventricular outflow tract and left ventricular intracavitary obstruction. A unique phenotype of hypertrophic cardiomyopathy with right ventricular outflow tract obstruction in conjunction with left ventricle intracavitary obstruction is discussed.
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