Neurofibromatosis Type 1 and Recurrent Metastatic Low-Grade Fibromyxoid Sarcoma: Case Report about a Rare Association

Neurofibromatosis type 1 is the most frequent phacomytosis. Patients with neurofibromatosis type 1 (NF1) have a high risk to develop benign or malignant tumors of neurogenic or non-neurogenic origin. The association of (NF1) to low-grade fibromyxoid sarcoma (LGFMS) is very rare. These tumors rarely develop at the skull and have a high incidence of local recurrence and distant metastasis. We report a case of occipital LGFMS in a patient diagnosed with NF1that developed a local and metastatic recurrence.