Why the study?
The Japanese Circulation Society recently updated diagnostic criteria to provide a methodology for diagnosing isolated cardiac sarcoidosis, but the characteristics of patients diagnosed using this approach needed assessment.
Does the diagnosis of isolated cardiac sarcoidosis using updated Japanese Circulation Society guidelines predict major adverse cardiovascular events in patients with suspected cardiac sarcoidosis?
Population
161 consecutive patients undergoing 18F-FDG PET for suspected cardiac sarcoidosis between 2012 and 2019
Comparison
Isolated cardiac sarcoidosis vs cardiac sarcoidosis with extracardiac involvement vs no cardiac sarcoidosis
Design
Retrospective cohort study
Follow-up
Median 522 days
Authors
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May warrant closer surveillance in isolated cardiac sarcoidosis; leaves open whether immunosuppression improves outcomes.
Does the diagnosis of isolated cardiac sarcoidosis using updated Japanese Circulation Society guidelines predict major adverse cardiovascular events in patients with suspected cardiac sarcoidosis?
Isolated cardiac sarcoidosis diagnosed via updated Japanese Circulation Society guidelines is associated with poor event-free survival and requires cautious management.
Sato et al. (2022) studied this question.
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