Why the study?
Does aorto-aortic bypass with growth-adjusted graft length and oestrogen height control prevent aortic reoperation and lower limb malperfusion in an infant with middle aortic syndrome and Marfan syndrome?
Does aorto-aortic bypass with growth-adjusted graft length and oestrogen height control prevent aortic reoperation and lower limb malperfusion in an infant with middle aortic syndrome and Marfan syndrome?
Aorto-aortic bypass with a growth-adjusted graft and subsequent oestrogen-mediated height control can provide durable long-term outcomes in infants with middle aortic syndrome and Marfan syndrome.
We present a 15-year follow-up after aorto-aortic bypass surgery in a 7-month-old infant with middle aortic syndrome and confirmed Marfan syndrome. In anticipation of her growth, the length of the graft was adjusted to the anticipated length of the narrowed aorta in her adolescence. In addition, her height was controlled by oestrogen, and her growth was stopped at 178 cm. To date, the patient is free from aortic reoperation and lower limb malperfusion.
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Heck et al. (2023) studied this question.
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