Key result
Advances in surgical techniques, such as sutureless repair, combined with aggressive catheter-based interventions and targeted medical therapies, have significantly improved survival rates for patients with pulmonary vein stenosis.
Why the study?
Pulmonary vein stenosis has historically had poor treatment results and a poorly understood pathophysiology.
A multidisciplinary approach utilizing advanced surgical, interventional, and medical therapies is shifting the prognosis of pediatric pulmonary vein stenosis from highly fatal to increasingly manageable.
May support multidisciplinary care in pediatric pulmonary vein stenosis; leaves open need for prospective trials to confirm benefits.
Pulmonary Vein Stenosis (PVS) is a rare disease with a prevalence of around 1. 7 cases per 100,000 children under 2 years old. Treatment options for this disease have not provided great results and pathophysiology of this condition is still poorly understood. Here, we will review the history of PVS including diagnostic tools and treatments, the current management approach, and what the future holds for this devastating disease.
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McLennan et al. (2021) conducted a review in Pulmonary Vein Stenosis. Advances in surgical techniques, such as sutureless repair, combined with aggressive catheter-based interventions and targeted medical therapies, have significantly improved survival rates for patients with pulmonary vein stenosis.
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