Why the study?
Aortic atresia is a rare congenital anomaly in adults that is difficult to differentiate from interrupted aortic arch without open surgery.
Demonstrates the feasibility of a 2-stage surgical approach for complex aortic atresia and associated anomalies in an adult.
Staged repair may be feasible in select adult aortic atresia cases; leaves open standardized diagnostic criteria and long-term outcomes.
Aortic atresia is a rare congenital vascular anomaly that occurs in adults. Differentiating it from interrupted aortic arch without open surgery is difficult. In some patients with type A interrupted aortic arches, aortic atresia may actually be caused by aortic coarctation. A 38-year-old man was diagnosed with aortic atresia, aortic regurgitation with a bicuspid valve, and aortic root enlargement. The surgery was performed in 2 stages. First stage: Descending aortic replacement with partial cardiopulmonary bypass without cardiac arrest. Second stage: Bentall procedure with mechanical valve replacement. We discuss the pathophysiology of interrupted aortic arch and aortic atresia in adults.
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Tokioka et al. (2025) studied this question.
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