January 1, 1995Pediatric Pathology & Laboratory Medicine
Case 5 Familial Right Ventricular Dysplasia (Cardiomyopathy)
Population
3 siblings with clinical evidence of a familial right ventricular cardiomyopathy
Design
Case_series
Authors
Discussion
Loading...
Member takes
Implication
May prompt family screening in RV dysplasia; hypothesis-generating without larger cohorts.
Structured PICO
P
Population
3 siblings with clinical evidence of a familial right ventricular cardiomyopathy
I
Intervention
Cardiac transplantation (in 2 siblings)
O
Outcome
Histopathologic findings in explanted hearts
This case series highlights the clinical presentation and histopathologic confirmation of familial right ventricular dysplasia in siblings, some of whom were successfully treated with cardiac transplantation.
Cite This Study
Kearney et al. (1995) studied this question.