Progressive Hemifacial Atrophy

Three cases of progressive hemifacial atrophy were studied. In two patients, abnormalities were noted on the computed tomographic (CT) brain scan, whereas a third patient, with widespread cutaneous and neurologic involvement, had a normal CT scan. Patient 1, first described 44 years ago, had a neurologic disorder with features that have previously been associated with progressive hemifacial atrophy, but that have appeared years after the hemifacial atrophy ceased progression.