Key result
Conservative management and assisted vaginal delivery with vacuum extraction led to a successful maternal outcome in a 22-year-old primigravida with Eisenmenger syndrome, despite a stillbirth.
Case Report (n=1)
Vaginal delivery with vacuum extraction and intensive care management can result in a successful maternal outcome in a pregnant patient newly diagnosed with Eisenmenger syndrome, despite the high mortality risk.
May inform individualized delivery planning in Eisenmenger syndrome; single case report leaves optimal strategies open.
Patients with Eisenmenger syndrome are advised against pregnancy. Sometimes patients are diagnosed with Eisenmenger syndrome for the first time during pregnancy. This is what has happened in our case. A primigravida was diagnosed with ventricular septal defect with severe pulmonary artery hypertension for the first time during pregnancy at 34 weeks period of gestation. Management of such patients is challenging with different studies showing variable results. Here we describe such a case which was managed conservatively and was allowed to go into labour spontaneously with vacuum extraction during second stage which subsequently led to a favourable maternal outcome.
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Chauhan et al. (2018) conducted a case report in Eisenmenger Syndrome in pregnancy (n=1). Conservative management and assisted vaginal delivery was evaluated on Maternal and fetal outcome. Conservative management and assisted vaginal delivery with vacuum extraction led to a successful maternal outcome in a 22-year-old primigravida with Eisenmenger syndrome, despite a stillbirth.
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