Key result
Stenting of both upper pulmonary veins in a patient with pulmonary vein stenosis from fibrosing mediastinitis resulted in a substantial reduction in pulmonary arterial pressure and improved symptoms.
Population
A 63-year-old man presenting with hemoptysis, progressive dyspnea, and fibrosing mediastinitis
Comparison
Stenting of both upper pulmonary veins
Design
Case report
Authors
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May support pulmonary vein stenting for fibrosing mediastinitis–related PH; hypothesis-generating and requires prospective confirmation.
Case Report (n=1)
Stenting of pulmonary veins can successfully treat pulmonary hypertension secondary to pulmonary vein stenosis from fibrosing mediastinitis, improving both hemodynamics and symptoms.
Ingraham et al. (2021) conducted a case report in Pulmonary vein stenosis from fibrosing mediastinitis (n=1). Stenting of upper pulmonary veins was evaluated on Hemodynamic and symptomatic improvement. Stenting of both upper pulmonary veins in a patient with pulmonary vein stenosis from fibrosing mediastinitis resulted in a substantial reduction in pulmonary arterial pressure and improved symptoms.
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