Key result
Systemic chemotherapy and radiation treat rare primary temporal bone Ewing sarcoma in a 5-month-old infant.
Case Report (n=1)
This case report documents an exceptionally rare presentation of primary Ewing sarcoma in the petrous temporal bone of a 5-month-old infant.
Multimodal chemo-radiation may be feasible in infantile petrous Ewing sarcoma; leaves open optimal regimens and long-term outcomes.
BACKGROUND: Primary Ewing sarcoma affecting the skull base in general and the petrous bone in particular is extremely rare with only 4 reports of Ewing sarcoma arising in the petrous temporal bone in the international medical literature. METHODS: The authors report for the first time a case of a primary Ewing sarcoma of the petrous temporal bone in a 5-month-old nursling, which became apparent with a complete peripheral facial palsy and ipsilateral surdity. RESULTS: The neoformation was treated by systemic chemotherapy and radiation of the tumor region. The diagnostic steps, therapy, and development of the child are described in detail; the literature concerning Ewing sarcoma originating from the skull in general and from the petrous temporal bone in particular is reviewed. CONCLUSIONS: The highlights of this case are an extremely uncommon location, an unusual age of presentation, as well as a unique set of symptoms.
No takes yet. Share an insight, caveat, or question.
Pfeiffer et al. (2006) conducted a case report in Primary Ewing sarcoma of the petrous temporal bone (n=1). Systemic chemotherapy and radiation was evaluated. Systemic chemotherapy and radiation were used to treat a 5-month-old nursling with an extremely rare primary Ewing sarcoma of the petrous temporal bone presenting with facial palsy and deafness.
Synapse has enriched 5 closely related papers on similar clinical questions. Consider them for comparative context: