Key result
Surgical repair of Ebstein's anomaly yields ~92% ten-year survival with acceptable long-term outcomes.
Why the study?
The study aimed to evaluate early and long-term outcomes following surgical correction of Ebstein's anomaly.
Observational (n=62)
No
Surgical treatment of Ebstein's anomaly demonstrates acceptable long-term survival and a low incidence of reinterventions.
Acceptable survival after Ebstein repair in this cohort; leaves open need for comparative trials to guide selection and timing.
OBJECTIVE: This study aimed to evaluate Ebstein's anomaly surgical correction and its early and long-term outcomes. METHODS: A retrospective analysis of 62 consecutive patients who underwent surgical repair of Ebstein's anomaly in our institution from January 2000 to July 2016. The following long-term outcomes were evaluated: survival, reoperations, tricuspid regurgitation, and postoperative right ventricular dysfunction. RESULTS: Valve repair was performed in 46 (74.2%) patients - 12 of them using the Da Silva cone reconstruction; tricuspid valve replacement was performed in 11 (17.7%) patients; univentricular palliation in one (1.6%) patient; and the one and a half ventricle repair in four (6.5%) patients. The patients' mean age at the time of surgery was 20.5±14.9 years, and 46.8% of them were male. The mean follow-up time was 8.8±6 years. The 30-day mortality rate was 8.06% and the one and 10-year survival rates were 91.9% both. Eleven (17.7%) of the 62 patients required late reoperation due to tricuspid regurgitation, in an average time of 7.1±4.9 years after the first procedure. CONCLUSION: In our experience, the long-term results of the surgical treatment of Ebstein's anomaly demonstrate an acceptable survival rate and a low incidence of reinterventions.
No takes yet. Share an insight, caveat, or question.
Silva et al. (2019) conducted an observational in Ebstein's anomaly (n=62). Surgical repair of Ebstein's anomaly was evaluated on 10-year survival rate. Surgical repair of Ebstein's anomaly demonstrated acceptable long-term outcomes, with 1- and 10-year survival rates of 91.9% and a 17.7% incidence of late reoperation.
Synapse has enriched one closely related paper. Consider it for comparative context: