Key result
Rare poorly differentiated endobronchial and mediastinal synovial sarcoma presents in a 15-year-old female.
Why the study?
Primary pulmonary and mediastinal synovial sarcomas are very uncommon, and heterogeneous clinical presentations make diagnosis challenging.
Case Report (n=1)
No
This case report highlights the rare presentation of primary endobronchial and mediastinal synovial sarcoma, emphasizing its radiologic and pathologic features.
Alerts clinicians to consider synovial sarcoma in rare pediatric mediastinal masses; hypothesis-generating pending larger series with molecular confirmation.
Primary thoracic synovial sarcomas (SS) typically occur as chest wall masses, although they rarely arise in the lung and pleura.Primary pulmonary and mediastinal SS is very uncommon in comparison with metastatic sarcoma and might arise in the tracheobronchial tree manifesting as an endoluminal mass, generally in adults.Signs and symptoms may additionally consist of wheezing, persistent pneumonia, bronchial asthma, chest ache, recurrent cough, atelectasis, hemoptysis, and weight loss.Because of the heterogeneity of signs and symptoms, clinical diagnosis may be tough.Herein, we present a case of primary endobronchial and mediastinal SS in a young female presenting with cough and expectoration associated with haemoptysis and breathlessness on exertion for 1week with particular emphasis on the radiologic and pathologic findings of this rare lesion.
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Krishna Kumar M (2022) conducted a case report in Primary endobronchial and mediastinal synovial sarcoma (n=1). Rigid bronchoscopy and endobronchial mass debulking was evaluated on Histopathological and immunohistochemical diagnosis. A 15-year-old female was diagnosed with a rare primary endobronchial and mediastinal poorly differentiated synovial sarcoma, though she was lost to follow-up before confirmatory translocation studies.
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