Adult Diagnosis of Swyer-James-Macleod Syndrome: A Rare Case Presentation

Swyer-James-MacLeod syndrome also known as unilateral hyperlucent lung syndrome is a rare entity associated with post infectious bronchiolitis obliterans occurring in childhood.It is characterized by hypoplasia and/or agenesis of the pulmonary arteries resulting in pulmonary parenchyma hypoperfusion.The diagnosis is usually made in childhood but sometimes occurs in adulthood.The disease often presents with dyspnea, decreased exercise tolerance, cough, hemoptysis, and recurrent pulmonary infections.SJMS may be confused with asthma or pulmonary embolism due to similar symptoms and may result in inappropriate therapy.Here we report a case of 26 year old female presented with cough, exertional breathlessness and fever for the past 8 months.She was diagnosed as SJMS on the basis of her medical history, clinical presentation and x-rays and computed tomography chest scan findings.