Key result
Prosthetic double-patch technique enables successful complete resection of a large RV fibroma.
Why the study?
Cardiac fibromas are rare benign cardiac tumors mostly in children, with very rare cases in adults, and limited data on surgical management in this population.
Case Report (n=1)
No
This case report demonstrates the successful surgical resection of a rare, large right ventricular fibroma in an adult patient using a prosthetic double-patch technique.
Supports feasibility of double-patch repair for rare adult RV fibroma; leaves open validation of durability and generalizability.
BACKGROUND: Cardiac fibromas are rare benign cardiac neoplasms, most frequently occurring in the pediatric population; with very rare cases identified in adults. The tumors are comprised of spindled cells with myofibroblastic ultrastructural features embedded in generally collagenous and elastic stroma. The tumors are intramural in the ventricles, most commonly the left ventricle. Clinical symptoms vary by location and size of tumor and some are asymptomatic. Surgical resection is curative, but rare cases require cardiac transplantation. CASE PRESENTATION: We report an asymptomatic, large, right ventricular fibroma in a 64-year-old woman. The patient underwent open incisional tumor biopsy via lower hemi-sternotomy, followed by complete tumor resection via full sternotomy a week later after confirming the tumor is benign. The tumor was resected using cardiopulmonary bypass, and the defect of right ventricular free wall was repaired using a prosthetic double-patch technique. The postoperative course was uneventful. The patient was discharged to home on day 4 post-complete tumor resection. CONCLUSION: This report expands the existing literature for better comprehension and detection of cardiac fibroma patients and also highlights the various imaging modalities, surgical management, and histological analysis.
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Ikegami et al. (2021) conducted a case report in Right ventricular cardiac fibroma (n=1). Surgical resection was evaluated on Successful tumor resection and postoperative recovery. Complete surgical resection of a large right ventricular cardiac fibroma using a prosthetic double-patch technique was successfully performed in a 64-year-old woman, resulting in an uneventful recovery.
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