Gelatinous Drop-like Dystrophy

A keratoplasty was performed on the right eye of a 12-year-old boy affected by gelatinous drop-like corneal dystrophy. This rare form of primary corneal amyloidosis has been more often reported in Japanese than in occidental literature. In the case presented here, the occasional fusiform deposits of amyloid observed in the stroma suggest a relationship between gelatinous drop-like corneal dystrophy and lattice dystrophy. A new classification of the different types of primary corneal amyloidosis is proposed.