Key result
Young man presents with severe heart failure linked to biventricular non-compaction, VSD, and aortic thoracic stenosis.
Why the study?
Non-compaction of the ventricular myocardium can be isolated or associated with other congenital anomalies, but controversies exist regarding right ventricular non-compaction due to its normal trabeculated morphology.
Case Report (n=1)
This case report highlights a rare presentation of biventricular non-compaction associated with a ventricular septal defect and descendent aortic stenosis.
Alerts clinicians to rare anomaly clusters in young heart failure; leaves open questions on pathogenesis and targeted therapies.
Non-compaction of the ventricular myocardium is a cardiomyopathy caused by the arrest of normal embryogenesis of the ventricles. It is classified in isolated non-compaction of the ventricles (most frequently of the left one) and in ventricular non-compaction associated with other congenital anomalies of the endocardium and myocardium, such as obstruction of the right or left ventricular outflow tracts, complex cyanotic congenital heart disease, and coronary artery anomalies. There are controversies regarding the right ventricle non-compaction due to the normally trabeculated shape of its walls. We present a case of severe heart failure with a complex anomaly: biventricular non-compaction, ventricular septal defect and aortic thoracic stenosis.
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S. Bradisteanu (2006) conducted a case report in Biventricular non-compaction, ventricular septal defect, and aortic thoracic stenosis (n=1). A young man presented with severe heart failure associated with a complex anomaly consisting of biventricular non-compaction, ventricular septal defect, and aortic thoracic stenosis.
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