Adrenocortical Carcinoma in a Young Patient: Report of a Rare Case and Review of the Literature at King Abdulaziz University Hospital

Adrenocortical tumors are rare neoplasms with poor prognosis and with an incidence of one in one million population. They are categorized as either functional (hormone-secreting) or silent and as either benign or malignant. We are reporting a very rare case of huge (16 cm) adrenocortical carcinoma in a 19-years-old male patient who presented with a progressively increasing right abdominal mass and uncontrolled systemic blood pressure for 2 years. Clinical exam was unremarkable for syndromic features. There was no history of precocious puberty. Imaging studies confirm the presence of a large right adrenal mass with malignant features. Laboratory tests including the hormonal work up were unremarkable. Endocrinology team was involved in the perioperative management of the patient followed by a complete surgical excision of the tumor. Patient tolerated the procedure and discharged in good condition. Follow up appointments confirm the stabilization of the blood pressure and general condition with no evidence of recurrence at 1-year post-resection.