Key result
Primary synovial sarcoma of the kidney is an extremely rare tumor in young adults, with fewer than 50 cases reported in the English literature, typically managed with surgery and chemotherapy.
Case Report (n=1)
Highlights the rare occurrence of primary synovial sarcoma in the kidney of a young adult, emphasizing the need for suspicion of malignancy in cystic renal masses.
May prompt suspicion for rare sarcoma in young adults with cystic renal masses; leaves optimal management open given <50 cases.
Synovial sarcoma (SS) is a soft tissue, generally deep seated neoplasms that occurs generally in the proximity of large joints. We report of a case of a 33-year-old man who was diagnosed with primary SS of the kidney which is an extremely rare tumor that accounts for less than 2% of malignant renal tumors. Contemporary management of renal synovial sarcoma includes surgical resection and ifosfamide-based chemotherapy and they remain the mainstay of therapy of synovial sarcoma, which is often applied, combined as part of an aggressive treatment approach. Fewer than 50 patients have been described in the English literature. Physicians should be aware of the possibility of malignancy in cystic renal masses and raise the suspicion of synovial sarcoma, especially when patients with renal masses are young adults. Along with the case report a literature review on primary synovial sarcomas of the kidney is provided with focus on the renal tumors' differential diagnosis.
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Abbas et al. (2014) conducted a case report in Primary synovial sarcoma of the kidney (n=1). Surgical resection and ifosfamide-based chemotherapy was evaluated. Primary synovial sarcoma of the kidney is an extremely rare tumor in young adults, with fewer than 50 cases reported in the English literature, typically managed with surgery and chemotherapy.
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