Key result
Anomalous mitral arcade variant causes acute heart failure, severe MR, and rapid fatal deterioration.
Why the study?
The anomalous mitral arcade is a rare congenital mitral valve malformation with limited data on variants presenting with acute decompensated heart failure in adults.
Case Report (n=1)
This case highlights a rare variant of anomalous mitral arcade that can remain asymptomatic until early adulthood before presenting with acute decompensated heart failure and rapid fatal deterioration.
Clinicians should consider anomalous mitral arcade in unexplained acute MR among young adults; extends known phenotypic spectrum of this rare congenital lesion.
The anomalous mitral arcade is a rare congenital malformation of the mitral valve and its tensor apparatus. It is characterized by enlarged papillary muscles connected to each other and to the free edge of the anterior mitral leaflet by a bridge of fibrous tissue. We report a rare variant of anomalous mitral arcade that was associated with accessory mitral leaflet in subaortic area and accessory chordae. Our patient was asymptomatic till the age of 18 years, when he presented for the first time in acute decompensated heart failure secondary to severe mitral regurgitation and left ventricular dysfunction. The patient had rapid deterioration with fatal outcome.
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Singh et al. (2013) conducted a case report in Anomalous mitral arcade variant with acute decompensated heart failure (n=1). Anomalous mitral arcade variant was evaluated. A rare variant of anomalous mitral arcade in an 18-year-old male led to acute decompensated heart failure, severe mitral regurgitation, and rapid fatal deterioration.
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