Key result
Systemic AL amyloidosis secondary to multiple myeloma drives rapid clinical deterioration in restrictive cardiomyopathy.
Why the study?
Amyloidosis is a rare disorder with multisystem involvement and non-specific symptoms that often delay diagnosis.
Case Report (n=1)
Answers are grounded in this paper and cite their sources.
Alerts clinicians to amyloidosis in unexplained restrictive cardiomyopathy; hypothesis-generating for early intervention impact.
Amyloidosis a rare disorder characterised by the deposition of amyloid protein aggregates in different organ systems throughout the body with resulting functional impairment of affected organs. It can present with localised or multisystemic deposits. Diagnosis is often delayed due to the non-specific nature of the symptoms. We present the case of a 59-year-old man with a 12-month history of non-specific symptoms. Investigations revealed Helicobacter pylori positive gastritis. Blood tests showed only a normocytic anaemia and thrombocytopaenia. CT scan showed proximal sigmoid thickening. Biopsies were unremarkable. Echocardiogram and cardiac MRI scan showed restrictive cardiomyopathy. Congo red staining of gastric biopsies showed amyloid deposition. The patient had elevated serum kappa light chains and a bone marrow biopsy confirmed multiple myeloma and he was subsequently diagnosed with systemic light chain (AL) amyloidosis secondary to this. He was started on chemotherapy and parenteral nutrition; however, he deteriorated rapidly and so was started on palliative treatment and discharged home.
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McFarlane et al. (2018) conducted a case report in Systemic light chain (AL) amyloidosis (n=1). A 59-year-old man with non-specific symptoms and restrictive cardiomyopathy was diagnosed with systemic light chain amyloidosis secondary to multiple myeloma and rapidly deteriorated.
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