Haematuria: A Rare Manifestation of Glanzmann Thrombasthenia

This is the authors' abstract. We don't add key points for this paper.

Summary: Glanzmann Thrombasthenia (GT) is a congenital thrombopathy characterised by bleeding manifestations that are sometimes severe. Treatment is based on platelet transfusions during bleeding. We report a case of TG revealed by haematuria and which presented a severe bleeding syndrome refractory to transfusions. Treatment with injections of recombinant activated factor VII was necessary. This case illustrates the value of using recombinant activated factor VII in TG in case of antiplatelet alloimmunisation or in case of lack of response to platelet transfusions.