Key result
MDCT and CMR delineate characteristic structural and functional hallmarks of isolated LV apical hypoplasia.
Why the study?
Isolated left ventricular apical hypoplasia is a unique cardiomyopathy with limited imaging characterization, necessitating detailed morphologic and functional assessment.
Case Report (n=1)
No
Facilitates noninvasive diagnosis of rare apical hypoplasia; extends sparse case-based imaging data without altering practice.
We report multidetector computed tomography (MDCT) and cardiac magnetic resonance (CMR) findings of a 34-year-old female with isolated left ventricular apical hypoplasia. The MDCT and CMR scans displayed a spherical left ventricle (LV) with extensive fatty infiltration within the myocardium at the apex, interventricular septum and inferior wall, anteroapical origin of the papillary muscle, right ventricle wrapping around the deficient LV apex, and impaired systolic function. MDCT visualized morphologic and also functional findings of this unique cardiomyopathy.
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Hong et al. (2016) conducted a case report in Isolated left ventricular apical hypoplasia (n=1). Multidetector computed tomography (MDCT) and cardiac magnetic resonance (CMR) was evaluated on Morphologic and functional characteristics of the heart. MDCT and CMR successfully visualized morphologic and functional findings of isolated left ventricular apical hypoplasia, including a spherical left ventricle, extensive fatty infiltration, and impaired systolic function.
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