Key result
Pericardiectomy yields steady clinical recovery without rehospitalization in rare carcinoid-related constrictive pericarditis.
Why the study?
Carcinoid heart disease rarely involves the pericardium, and constrictive pericarditis due to metastatic carcinoid disease is an exceptionally rare presentation.
Case Report (n=1)
May support pericardiectomy in carcinoid constrictive pericarditis; leaves open need for larger studies to confirm benefit.
We describe a case of atypical carcinoid heart disease. A 62-year-old woman with well-differentiated neuroendocrine tumor metastatic to the liver and lymph nodes presented with recurrent unilateral pleural effusions and lower extremity edema. Multimodality imaging and workup resulted in the diagnosis of carcinoid-related constrictive pericarditis, a rare form of carcinoid heart disease. (Level of Difficulty: Intermediate.)
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Wang et al. (2020) conducted a case report in Carcinoid constrictive pericarditis (n=1). Pericardiectomy was evaluated on Clinical improvement. Pericardiectomy led to steady clinical improvement without recurrent hospitalizations in a 62-year-old woman with a rare presentation of carcinoid-related constrictive pericarditis.
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