Key result
Primary sutureless repair enables ECMO weaning and unobstructed pulmonary venous flow in neonatal common pulmonary vein atresia.
Why the study?
Common pulmonary vein atresia is an extremely rare and lethal congenital heart defect with limited reports of successful surgical repair using sutureless technique.
Does primary sutureless repair combined with early VA-ECMO support improve survival and prevent anastomotic obstruction in a neonate with common pulmonary vein atresia?
Case Report (n=1)
No
Does primary sutureless repair combined with early VA-ECMO support improve survival and prevent anastomotic obstruction in a neonate with common pulmonary vein atresia?
Early primary sutureless repair with immediate postoperative VA-ECMO support is a feasible and successful therapeutic strategy for the highly lethal neonatal common pulmonary vein atresia.
Supports primary sutureless repair as a potential option in CPVA; hypothesis-generating and requires validation before practice change.
Common pulmonary vein atresia (CPVA) is an extremely rare and lethal congenital heart defect characterized by the absence of a functional connection between the common pulmonary vein chamber (CPVC) and both the left atrium and systemic venous system. We report a case of a full-term female infant who successfully underwent primary sutureless repair. The patient developed acute respiratory distress syndrome (ARDS) with severe cyanosis and refractory hypoxemia 12 min after birth and underwent emergent surgery at 15 h of life. Intraoperative findings confirmed CPVA with bilateral superior pulmonary vein stenosis. Sutureless anastomosis was performed, leaving a 2.5 mm interatrial communication. Due to severe pulmonary hypertension and high-dose vasoactive requirements, venoarterial extracorporeal membrane oxygenation (VA-ECMO) support was established immediately. ECMO was weaned on postoperative day 6, the patient was extubated on day 10, and discharged on day 43. Two-month follow-up showed unobstructed pulmonary venous flow without evidence of anastomotic stenosis. To our knowledge, this is the first report of successful primary sutureless repair of this cardiac malformation.
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Zheng et al. (2026) conducted a case report in Common pulmonary vein atresia (CPVA) (n=1). Primary sutureless repair with interatrial shunt preservation and postoperative VA-ECMO was evaluated on Survival and pulmonary venous flow patency. Primary sutureless repair in a 15-hour-old neonate with common pulmonary vein atresia resulted in successful weaning from ECMO and unobstructed pulmonary venous flow at 2-month follow-up.
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