Key result
Gastrostomy surgery triggers sudden cardiac arrest and hemodynamic collapse in advanced Duchenne cardiomyopathy.
Why the study?
The increased life expectancy of DMD patients due to respiratory therapy has raised challenges in managing advanced cardiomyopathy during anesthesia.
Case Report (n=1)
Anesthesia in advanced DMD cardiomyopathy warrants arrest preparedness; this single case leaves open optimal protocols for high-risk procedures.
Duchenne muscular dystrophy (DMD) is a progressive myopathy. The development of respiratory therapy has increased the life expectancy of DMD patients. This change has increased the chances of anesthesia administration in DMD patients with advanced cardiomyopathy. We report a severe cardiomyopathy case in a 14-year-old boy with DMD, adrenal insufficiency, and severe mental retardation, who experienced a sudden cardiac arrest with successful resuscitation. The patient underwent feeding gastrostomy surgery to relieve recurrent aspiration pneumonia, during which cardiac index and heart rate decreased. Cardiomyopathy has emerged as a new challenge in DMD patients; it is important to maintain end organ perfusion by proper function of the left ventricle.
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Park et al. (2018) conducted a case report in Duchenne muscular dystrophy with advanced cardiomyopathy (n=1). Anesthesia and feeding gastrostomy surgery was evaluated on Sudden cardiac arrest and hemodynamic changes. Feeding gastrostomy surgery in a 14-year-old boy with Duchenne muscular dystrophy and advanced cardiomyopathy was complicated by sudden cardiac arrest and decreased cardiac index.
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