Key result
Single-stage repair successfully treats right circumflex aorta with ventricular septal defect in a toddler.
Why the study?
Right circumflex aorta is a rare congenital vascular anomaly with very few reported cases, and the majority of cases present without any intracardiac defects.
Case Report (n=1)
This case report demonstrates the feasibility of a single-stage surgical repair for the rare combination of a right circumflex aorta and ventricular septal defect in a pediatric patient.
Answers are grounded in this paper and cite their sources.
May inform rare right circumflex aorta cases with VSD; extends sparse case reports but leaves generalizability open.
The right circumflex aorta, also called circumflex retroesophageal right aortic arch, is a rare congenital vascular anomaly. It accounts for less than 0.1 % of the vascular rings, which themselves encompass only 1%–3% of all congenital heart diseases. It is caused by a right aortic arch with a left ligamentum arteriosum and left descending aorta. The majority of cases present without any intracardiac defects. Very few cases of right circumflex aorta were reported in the literature. We present a case of 2-year-old child with right circumflex aorta associated with a ventricular septal defect, who underwent successful single-stage repair.
No takes yet. Share an insight, caveat, or question.
Yadav et al. (2026) conducted a case report in Right circumflex aorta with ventricular septal defect (n=1). Single-stage surgical repair was evaluated on Successful single-stage repair. Single-stage surgical repair was successfully performed in 1 child (2 years old) with a right circumflex aorta and associated ventricular septal defect.
Synapse has enriched 10 related papers. Consider them for comparative context: