Dental Implications of Parry-Romberg Syndrome: A Case of Progressive Hemifacial Atrophy

Parry-Romberg syndrome (PRS) is a rare degenerative disorder of unknown origin that causes slow, progressive atrophy usually on left side of the face. The cause may be associated with a malfunction of the sympathetic nervous system, with or without neurological symptoms. Atrophy usually begins in first and second decades of life and progresses gradually over several years. There is no definitive management for this condition, but once the condition is stabilized, reconstructive surgery of the damaged skin and soft tissue can correct the disproportion. Additionally, with the extensive systemic involvement in such a condition, a multidisciplinary approach is needed because of its devastating effects on the entire body, treatment requires a multidisciplinary approach. Further research is needed to clearly understand the etiology and provide patients with accurate treatment plans. The cause of PRS is unknown however certain resources mention its relation to autoimmune conditions. A multidisciplinary approach is essential in such patients to enhance their quality of life. The objective of this article is to present an insight into the etiology of PRS with a case report of a 9-year-old male patient, who was diagnosed with PRS and developed progressive hemifacial atrophy without neurological manifestations.