Cardiovascular magnetic resonance in the evaluation of congenitally corrected transposition of the great arteries

Congenitally corrected transposition of the great arteries (ccTGA), is a rare cardiac anomaly (occurring in less than 1% of all congenital heart diseases) characterised by atrio-ventricular and ventricular-arterial discordance. We report on a 13-year-old female with situs inversus totalis, ccTGA, peri-membranous VSD, and sub-PS presenting with worsening fatigue on physical exertion, excessive sweating, and intermittent palpitations not associated with physical activity. Echocardiography was used in diagnosis. CMR revealed mild systolic impairment (ejection fraction, EF 55%) of the systemic ventricle (morphologic RV), a perimembranous VSD, flattening of the interventricular septum in systole and diastole, indicative of pressure and volume overload, respectively.