Key result
Multimodality imaging establishes late-presenting CCTGA and severe systemic RV failure in acute heart failure.
Why the study?
Congenitally corrected transposition of the great arteries is a rare congenital anomaly that often leads to progressive systemic right ventricular dysfunction and heart failure in adulthood, requiring early recognition and comprehensive imaging for management.
Case Report (n=1)
Multimodality imaging is critical for the accurate diagnosis and management of rare congenital anomalies like CCTGA that can present as progressive heart failure in adulthood.
Case report underscores potential of multimodality imaging in adult ccTGA heart failure; leaves open systematic evaluation.
Congenitally corrected transposition of the great arteries (CCTGA) is a rare congenital anomaly characterized by atrioventricular and ventriculoarterial discordance, in which the morphologic right ventricle supports systemic circulation, often leading to progressive dysfunction and heart failure in adulthood. We report the case of a 33-year-old man presenting with progressively worsening dyspnea. Chest radiography demonstrated cardiomegaly with dextrocardia and features of pulmonary interstitial edema. Multimodality imaging—including transthoracic echocardiography, coronary CT angiography, and cardiac MRI—was essential in confirming CCTGA and assessing secondary right ventricular failure. This case highlights the critical role of early recognition and comprehensive imaging in guiding management and optimizing outcomes in adult patients with this rare congenital condition.
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Wongpen et al. (2026) conducted a case report in Congenitally corrected transposition of the great arteries (CCTGA) (n=1). Multimodality cardiac imaging was evaluated on Diagnosis of CCTGA and assessment of right ventricular failure. Multimodality imaging successfully confirmed the diagnosis of congenitally corrected transposition of the great arteries and severe right ventricular cardiomyopathy in an adult presenting with acute heart failure.
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