Unilateral Renal Agenesis, Think in Zinner Syndrome

Zinner syndrome is indeed a rare congenital condition characterized by urogenital system malformation, specifically involving abnormalities of the mesonephric/Wolffian duct. It typically presents with the triad of unilateral renal agenesis, ipsilateral seminal vesicle cyst, and ipsilateral ejaculatory duct obstruction. We present a case of an 8-year-old male child with a prenatal diagnosis of solitary kidney (right renal agenesis) and the subsequent identification of a globose right seminal vesicle with a cystic appearance. This finding is consistent with Zinner syndrome.