Key result
Central VA-ECMO followed by HeartMate III LVAD implantation successfully managed refractory cardiac decompensation in a 14-year-old girl with Naxos syndrome.
Why the study?
Advanced heart failure in inherited arrhythmogenic cardiomyopathies poses significant therapeutic challenges, particularly in pediatric patients with rare forms such as Naxos syndrome where mechanical circulatory support may be required.
Population
One 14-year-old girl with Naxos syndrome and refractory cardiac decompensation complicated by malignant ventricular arrhythmia
Comparison
Central VA-ECMO followed by HeartMate III LVAD implantation
Design
Case report
Authors
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Central VA-ECMO may be considered to bridge pediatric Naxos syndrome to durable LVAD; extends options in rare inherited arrhythmogenic cardiomyopathies.
Case Report (n=1)
Central VA-ECMO can serve as an effective bridge to durable LVAD support in pediatric patients with complex inherited arrhythmogenic cardiomyopathies like Naxos syndrome.
Akdi et al. (2026) conducted a case report in Naxos syndrome with decompensated heart failure (n=1). Central veno-arterial extracorporeal membrane oxygenation (VA-ECMO) and HeartMate III LVAD was evaluated. Central VA-ECMO followed by HeartMate III LVAD implantation successfully managed refractory cardiac decompensation in a 14-year-old girl with Naxos syndrome.
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