Why the study?
Patients with pulmonary hypertension associated with congenital heart disease represent an increasingly complex population, yet consensus recommendations on optimal management and referral timing were lacking.
This American Heart Association scientific statement provides comprehensive guidance on the evaluation, management, and future research directions for patients with pulmonary hypertension associated with congenital heart disease.
Guides evaluation and management of PH in congenital heart disease; extends prior statements by addressing disparities and research gaps.
Patients with pulmonary hypertension associated with congenital heart disease make up an increasing proportion of the total pulmonary hypertension population who bring with them added complexity because of underlying anatomical and hemodynamic abnormalities. Currently, no consensus recommendations are available on how to best manage this group of patients for either the primary cardiologist or pulmonary hypertension subspecialist, including timing of referral. The purposes of this document are (1) to describe the various pulmonary hypertension groups and subgroups associated with congenital heart disease, (2) to describe imaging modalities used in patient evaluation, (3) to elucidate medical and surgical management considerations, (4) to highlight disparities within this population, and (5) to identify gaps and future research needs of patients with pulmonary hypertension associated with congenital heart disease.
No takes yet. Share an insight, caveat, or question.
Jone et al. (2023) studied this question.
Synapse has enriched 5 closely related papers on similar clinical questions. Consider them for comparative context: