Key result
An infant with congenital long QT syndrome successfully underwent implantable cardioverter-defibrillator placement after resuscitation from sudden cardiac arrest.
Case Report (n=1)
No
This case report highlights the anesthetic considerations and feasibility of ICD placement in an infant with congenital long QT syndrome following sudden cardiac arrest.
May support feasibility of infant ICD placement in congenital long QT syndrome; hypothesis-generating and should not yet change practice.
Sudden cardiac arrest (SCA) in children is a rare, but catastrophic event. Children with cardiac pathology at particular risk include those with congenital long QT syndrome (CLQTS) and hypertrophic cardiomyopathy. CLQTS is a genetic disorder of the cardiac ion channels and is associated with significant risk of malignant ventricular arrhythmias and SCA. For symptomatic, untreated patients, the mortality rate is approximately 20% for the first year and 50% at ten years. Use of an implantable cardioverter-defibrillator (ICD) is recommended for the prevention of SCA in this patient population. We report a case of CLQTS, who after successful resuscitation from SCA, underwent ICD placement at our center.
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Kansara et al. (2011) conducted a case report in Congenital long QT syndrome (CLQTS) (n=1). Implantable cardioverter-defibrillator (ICD) placement was evaluated. An infant with congenital long QT syndrome successfully underwent implantable cardioverter-defibrillator placement after resuscitation from sudden cardiac arrest.
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